Olivopontocerebellar atrophy-deafness syndrome
Olivopontocerebellar atrophy-deafness syndrome is a rare genetic disorder characterized by olivopontocerebellar atrophy which begins in infancy, sensorineural hearing loss, and speech delay. Additional findings include cerebellar ataxia.
Source: Wikipedia — Olivopontocerebellar atrophy-deafness syndrome (CC BY-SA 4.0)